1 Jan 2009Case Report
Acute abdomen for perforated gastrointestinal stromal tumor( GIST). A case report
Antonino Versaci 1Antonio Macrì 1Maddalena Grosso 2Marialuisa Terranova 3Grazia Leonello 3Antonio Ieni 4Giovanna Rivoli 3Ciro Famulari 3
Affiliations
Article Info
1 Dipartimento di Patologia Umana dell’Università di Messina
2 Cattedra di Anatomia Patologica, Dipartimento di Patologia Umana dell’Università di Messina
3 Cattedra di Chirurgia d’Urgenza e Trapianti d’Organo, Dipartimento di Patologia Umana dell’Università di Messina
4 Cattedra di Anatomia Patologica,Dipartimento di Patologia Umana dell’Università di Messina
Ann. Ital. Chir., 2009, 80(1), 68-74;
Published: 1 Jan 2009
Copyright © 2009 Annali Italiani di Chirurgia
This work is licensed under a Creative Commons Attribution 4.0 International License.
Abstract
The authors report on a case of voluminous perforated gastrointestinal stromal tumor (GIST) of small intestine and make a review to the light of most recent clinicopathologic advancements. The first clinical manifestation as acute abdomen due to their perforation extremely rare. Gastrointestinal stromal tumor (GIST) represent a rare group of multiforms tumors with various biological behaviour. Were identified in the past as leiomyomas, leiomyosarcomas or leiomyoblastomas, has been reclassificated on immunochemical features, with a positive expression of Kit (CD117 antigen). Traditionally the prognostic factors of these tumour are: mitotic rate, tumor size and anatomic site. The complete surgical resection and use of imatinib mesylate (Gleevec) are the best available approach.
Keywords
- Acute abdomen
- CD117
- Gastrointestinal stromal tumors (GISTs)
- Perforation